Progressive maculopathy in a child resulting from vitreopapillary traction on a congenitally anomalous nerve
Progressive maculopathy in a child resulting from vitreopapillary traction on a congenitally anomalous nerve

Progressive maculopathy in a child resulting from vitreopapillary traction on a congenitally anomalous nerve

Retin Cases Brief Rep. 2024 Oct 7. doi: 10.1097/ICB.0000000000001666. Online ahead of print.

ABSTRACT

PURPOSE: To present a case of worsening maculopathy and vision loss due to vitreopapillary traction associated with an anomalous optic nerve head in a pediatric patient successfully managed with pars plana vitrectomy.

METHODS: Retrospective case report.

RESULTS: A 13-year-old boy presented with unilateral maculopathy that slowly progressed over a four-year period. As his visual acuity declined, he became increasingly symptomatic. The macular pathology occurred in the setting of vitreopapillary traction overlying multiple congenital optic nerve abnormalities, including a myelinated nerve fiber layer and a Bergmeister papilla. Following pars plana vitrectomy to alleviate the traction, the patient’s macular appearance improved, and his vision slowly recovered to baseline.

CONCLUSION: There are limited reports of congenital optic nerve anomalies associated with vitreopapillary traction and maculopathy among any age group. This report illustrates a pediatric case in which removal of traction on the nerve head by pars plana vitrectomy was the key therapeutic intervention to alleviate the maculopathy.

PMID:39405500 | DOI:10.1097/ICB.0000000000001666