A Unique Case of Pure Bilateral Lambdoid Craniosynostosis and Progression to Mercedes-Benz Syndrome Following Spring Cranioplasty
A Unique Case of Pure Bilateral Lambdoid Craniosynostosis and Progression to Mercedes-Benz Syndrome Following Spring Cranioplasty

A Unique Case of Pure Bilateral Lambdoid Craniosynostosis and Progression to Mercedes-Benz Syndrome Following Spring Cranioplasty

Cleft Palate Craniofac J. 2025 Oct 25:10556656251389537. doi: 10.1177/10556656251389537. Online ahead of print.

ABSTRACT

We report a case of a 3-month-old female with isolated bilateral lambdoid craniosynostosis treated by suturectomy with cranial springs, who later demonstrated unexpected sagittal fusion. The patient presented with bilateral lambdoid and mendosal fusion producing a distinctive posterior vault deformity. Springs placed at suturectomy were removed five months later. Segmented CT analysis revealed intracranial volume expansion from 727.4 cm3 pre-op to 1371.9 cm3 post-removal, with minimal blood loss and uncomplicated recovery. Post-removal imaging showed complete sagittal synostosis, suggesting either a delayed manifestation of Mercedes-Benz pattern synostosis or a mechanically induced secondary synostosis due to springs, warranting further investigation.

PMID:41138267 | DOI:10.1177/10556656251389537